ID

45985

Beschreibung

Principal Investigator: Nicholas O. Davidson, MD, Washington University, St. Louis, MO, USA MeSH: Familial Adenomatous Polyposis,Colonic Neoplasms https://www.ncbi.nlm.nih.gov/projects/gap/cgi-bin/study.cgi?study_id=phs000904 The ~80% of individuals with classic familial adenomatous polyposis (FAP) have detectable mutations in the coding sequence of the adenomatous polyposis coli (APC) gene. To investigate the 20% of families without detectable causative mutations, we used exome sequencing and second-generation sequencing of the APC locus including non-coding regions. We identified a novel ~11kb deletion 44kb upstream of APC that was present only in affected individuals of three kindreds. SNP analysis showed that this ~11kb deletion was accompanied by silencing of one of the APC alleles in blood-derived RNA of affected individuals.

Link

dbGaP study=phs000904

Stichworte

  1. 06.04.24 06.04.24 - Madita Rudolph
Rechteinhaber

Nicholas O. Davidson, MD, Washington University, St. Louis, MO, USA

Hochgeladen am

6. April 2024

DOI

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Lizenz

Creative Commons BY 4.0

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dbGaP phs000904 APC Promoter Deletion in Classic Familial Adenomatous Polyposis

Eligibility Criteria

Inclusion and exclusion criteria
Beschreibung

Inclusion and exclusion criteria

Alias
UMLS CUI [1,1]
C1512693
UMLS CUI [1,2]
C0680251
*Inclusion Criteria:* Individuals with classic familial adenomatous polyposis were tested for known APC mutations with Colaris AP® (Myriad Genetic Laboratories). Those without detectable mutations by Colaris AP® and consenting family members were enrolled.
Beschreibung

Elig.phs000904.v1.p1.1

Datentyp

boolean

Alias
UMLS CUI [1,1]
C1512693
UMLS CUI [1,2]
C0032580
UMLS CUI [1,3]
C4522286
UMLS CUI [1,4]
C0039593
UMLS CUI [2,1]
C1512693
UMLS CUI [2,2]
C0021430
UMLS CUI [2,3]
C0086282
*Exclusion Criteria:* Individuals with sporadic gastrointestinal cancer or a family history of cancer not suggestive of hereditary or familial diseases were excluded.
Beschreibung

Elig.phs000904.v1.p1.2

Datentyp

boolean

Alias
UMLS CUI [1,1]
C0680251
UMLS CUI [1,2]
C0685938
UMLS CUI [1,3]
C0205422
UMLS CUI [2,1]
C0680251
UMLS CUI [2,2]
C0260515
UMLS CUI [2,3]
C0019247
UMLS CUI [2,4]
C1272460

Ähnliche Modelle

Eligibility Criteria

Name
Typ
Description | Question | Decode (Coded Value)
Datentyp
Alias
Item Group
Inclusion and exclusion criteria
C1512693 (UMLS CUI [1,1])
C0680251 (UMLS CUI [1,2])
Elig.phs000904.v1.p1.1
Item
*Inclusion Criteria:* Individuals with classic familial adenomatous polyposis were tested for known APC mutations with Colaris AP® (Myriad Genetic Laboratories). Those without detectable mutations by Colaris AP® and consenting family members were enrolled.
boolean
C1512693 (UMLS CUI [1,1])
C0032580 (UMLS CUI [1,2])
C4522286 (UMLS CUI [1,3])
C0039593 (UMLS CUI [1,4])
C1512693 (UMLS CUI [2,1])
C0021430 (UMLS CUI [2,2])
C0086282 (UMLS CUI [2,3])
Elig.phs000904.v1.p1.2
Item
*Exclusion Criteria:* Individuals with sporadic gastrointestinal cancer or a family history of cancer not suggestive of hereditary or familial diseases were excluded.
boolean
C0680251 (UMLS CUI [1,1])
C0685938 (UMLS CUI [1,2])
C0205422 (UMLS CUI [1,3])
C0680251 (UMLS CUI [2,1])
C0260515 (UMLS CUI [2,2])
C0019247 (UMLS CUI [2,3])
C1272460 (UMLS CUI [2,4])

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