ID

45909

Beschreibung

Principal Investigator: Bernice Morrow, PhD, Albert Einstein College of Medicine, Bronx, NY, USA MeSH: Bilateral deafness https://www.ncbi.nlm.nih.gov/projects/gap/cgi-bin/study.cgi?study_id=phs000969 Our goal is to find genes responsible for non-syndromic sensorineural hearing loss. Blood samples were collected from the JS6 family affected with hearing loss. The family is of Caribbean Hispanic ethnicity. Family JS6 consisted of two deaf siblings, JS6.001 (Male) and JS6.002 (Female) and healthy parents, JS6.100 (mother) and JS6.200 (father). The siblings had no other medical findings. Audiometry tests and Rinne and Weber tuning fork tests identified sensorineural hearing loss in the two siblings. We performed whole exome sequencing of the four individuals and identified a recessive mutation, p.(Arg186Trp), in the CIB2 gene in the two affected siblings. Both parents were unaffected carriers.

Link

dbGaP study = phs000969

Stichworte

  1. 17.01.24 17.01.24 - Simon Heim
Rechteinhaber

Bernice Morrow, PhD, Albert Einstein College of Medicine, Bronx, NY, USA

Hochgeladen am

17. Januar 2024

DOI

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Lizenz

Creative Commons BY 4.0

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dbGaP phs000969 Whole Exome Sequence of Hearing Loss Family

Eligibility Criteria

Inclusion and exclusion criteria
Beschreibung

Inclusion and exclusion criteria

Alias
UMLS CUI [1,1]
C1512693
UMLS CUI [1,2]
C0680251
*Inclusion criteria*: More than one affected family member with congenital deafness. Both affected siblings and normal parents were available for DNA collection.
Beschreibung

*Inclusion criteria*: More than one affected family member with congenital deafness. Both affected siblings and normal parents were available for DNA collection.

Datentyp

boolean

Alias
UMLS CUI [1,1]
C1512693
UMLS CUI [1,2]
C5142998
UMLS CUI [1,3]
C0392760
UMLS CUI [1,4]
C0086282
UMLS CUI [1,5]
C0339789
UMLS CUI [2,1]
C1512693
UMLS CUI [2,2]
C0470187
UMLS CUI [2,3]
C0037047
UMLS CUI [2,4]
C0392760
UMLS CUI [2,5]
C0030551
UMLS CUI [2,6]
C0200345
UMLS CUI [2,7]
C0012854
*Exclusion criteria*: Normal hearing in all family members. Or parents were unavailable for DNA sequencing.
Beschreibung

*Exclusion criteria*: Normal hearing in all family members. Or parents were unavailable for DNA sequencing.

Datentyp

boolean

Alias
UMLS CUI [1,1]
C0680251
UMLS CUI [1,2]
C0234725
UMLS CUI [1,3]
C0086282
UMLS CUI [2,1]
C0680251
UMLS CUI [2,2]
C0030551
UMLS CUI [2,3]
C0686905
UMLS CUI [2,4]
C0687728

Ähnliche Modelle

Eligibility Criteria

Name
Typ
Description | Question | Decode (Coded Value)
Datentyp
Alias
Item Group
Inclusion and exclusion criteria
C1512693 (UMLS CUI [1,1])
C0680251 (UMLS CUI [1,2])
*Inclusion criteria*: More than one affected family member with congenital deafness. Both affected siblings and normal parents were available for DNA collection.
Item
*Inclusion criteria*: More than one affected family member with congenital deafness. Both affected siblings and normal parents were available for DNA collection.
boolean
C1512693 (UMLS CUI [1,1])
C5142998 (UMLS CUI [1,2])
C0392760 (UMLS CUI [1,3])
C0086282 (UMLS CUI [1,4])
C0339789 (UMLS CUI [1,5])
C1512693 (UMLS CUI [2,1])
C0470187 (UMLS CUI [2,2])
C0037047 (UMLS CUI [2,3])
C0392760 (UMLS CUI [2,4])
C0030551 (UMLS CUI [2,5])
C0200345 (UMLS CUI [2,6])
C0012854 (UMLS CUI [2,7])
*Exclusion criteria*: Normal hearing in all family members. Or parents were unavailable for DNA sequencing.
Item
*Exclusion criteria*: Normal hearing in all family members. Or parents were unavailable for DNA sequencing.
boolean
C0680251 (UMLS CUI [1,1])
C0234725 (UMLS CUI [1,2])
C0086282 (UMLS CUI [1,3])
C0680251 (UMLS CUI [2,1])
C0030551 (UMLS CUI [2,2])
C0686905 (UMLS CUI [2,3])
C0687728 (UMLS CUI [2,4])

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