ID

45673

Beschrijving

Principal Investigator: Kwok-wai Lo, Chinese University of Hong Kong, Hong Kong, China MeSH: Nasopharyngeal Neoplasms https://www.ncbi.nlm.nih.gov/projects/gap/cgi-bin/study.cgi?study_id=phs001244 Nasopharyngeal carcinoma (NPC) is an aggressive head and neck cancer characterized by Epstein-Barr virus (EBV) infection and dense lymphocyte infiltration. The scarcity of NPC genomic data hinders the understanding of NPC biology, disease progression, and rational therapy design. Here, we performed whole-exome sequencing (WES) on 111 micro-dissected EBV-positive NPCs, with 15 cases subjected to further whole-genome sequencing (WGS), to determine its mutational landscape. We identified enrichment for genomic aberrations of multiple negative regulators of the NF-kB pathway in a total of 41% of cases including CYLD, TRAF3, NFKBIA and NLRC5. Functional analysis confirmed novel inactivating CYLD mutations as drivers for NPC cell growth. The EBV oncoprotein latent member protein 1 (LMP1) functions to constitutively activate NF-kB signaling, and we observed mutual exclusivity among somatic NF-kB pathway aberrations and LMP1-overexpression, suggesting that NF-kB activation is selected for by both somatic and viral events during NPC pathogenesis.

Link

dbGaP study = phs001244

Trefwoorden

  1. 06-04-23 06-04-23 - Simon Heim
Houder van rechten

Kwok-wai Lo, Chinese University of Hong Kong, Hong Kong, China

Geüploaded op

6 april 2023

DOI

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Licentie

Creative Commons BY 4.0

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dbGaP phs001244 Nasopharynx Cancer Whole Exome Sequencing

Eligibility Criteria

Inclusion and exclusion criteria
Beschrijving

Inclusion and exclusion criteria

Alias
UMLS CUI [1,1]
C1512693
UMLS CUI [1,2]
C0680251
Subjects were selected on the basis of biopsy proven nasopharynx cancer and restricted to treatment naive individuals. In cases where multiple tumors were available these were included.
Beschrijving

Subjects were selected on the basis of biopsy proven nasopharynx cancer and restricted to treatment naive individuals. In cases where multiple tumors were available these were included.

Datatype

boolean

Alias
UMLS CUI [1,1]
C0949542
UMLS CUI [1,2]
C0005558
UMLS CUI [1,3]
C0238301
UMLS CUI [1,4]
C0443288
UMLS CUI [1,5]
C5395609

Similar models

Eligibility Criteria

Name
Type
Description | Question | Decode (Coded Value)
Datatype
Alias
Item Group
Inclusion and exclusion criteria
C1512693 (UMLS CUI [1,1])
C0680251 (UMLS CUI [1,2])
Subjects were selected on the basis of biopsy proven nasopharynx cancer and restricted to treatment naive individuals. In cases where multiple tumors were available these were included.
Item
Subjects were selected on the basis of biopsy proven nasopharynx cancer and restricted to treatment naive individuals. In cases where multiple tumors were available these were included.
boolean
C0949542 (UMLS CUI [1,1])
C0005558 (UMLS CUI [1,2])
C0238301 (UMLS CUI [1,3])
C0443288 (UMLS CUI [1,4])
C5395609 (UMLS CUI [1,5])

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