0 Beoordelingen

ID

45630

Beschrijving

Principal Investigator: Matt Zinter, MD, University of California, San Francisco, San Francisco, CA, USA MeSH: Bone Marrow Transplantation,Hematopoietic Stem Cell Transplantation,Graft vs Host Disease,Myocarditis https://www.ncbi.nlm.nih.gov/projects/gap/cgi-bin/study.cgi?study_id=phs001336 We report the case of a 15-year-old female with hypodiploid pre-B acute lymphoblastic leukemia status post allogeneic hematopoietic stem cell transplantation (HCT) from a matched unrelated male donor who presented on transplant day +75 with cardiac arrest due to ventricular fibrillation associated with fulminant myocarditis. Using conventional diagnostics, an exhaustive search for microbial pathogens in the heart biopsy as well as nasopharynx, blood, urine, and endotracheal aspirate was performed but did not uncover a candidate pathogen. The family consented to a research study for the use of unbiased next-generation genomic sequencing for pathogen identification in the myocardial biopsy. DNA sequencing was performed on 1.5 x 10sup8/sup sequencing pairs and no microbial pathogens were identified. Interestingly, a significant component of Y-chromosomal human DNA was identified, suggesting infiltration of at least 10 donor leukocytes per host cell. This finding is grossly consistent with the lymphocyte:myocyte ratio in the biopsy according to visual inspection at 40x magnification. This case merits discussion due to (1) her survival after 17 days of veno-arterial extracorporeal life support (ECLS) and (2) the possibility of cardiotropic graft versus host disease (GVHD).

Link

dbGaP study = phs001336

Trefwoorden

  1. 02-03-23 02-03-23 - Simon Heim
Houder van rechten

Matt Zinter, MD, University of California, San Francisco, San Francisco, CA, USA

Geüploaded op

2 maart 2023

DOI

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Licentie

Creative Commons BY 4.0

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    dbGaP phs001336 ECLS Survival in Pediatric HCT Recipient with Presumed Cardiac GVHD

    The subject consent data table contains patient IDs, consent group information, and affection status of subject for hypodiploid pre-B acute lymphoblastic leukemia status post matched unrelated donor allogeneic hematopoietic stem cell transplant complicated by fulminant myocarditis on day +75.

    pht006204
    Beschrijving

    pht006204

    Alias
    UMLS CUI [1,1]
    C3846158 (Other Coding)
    LOINC
    LA4728-7
    Subject ID
    Beschrijving

    PatientID

    Datatype

    string

    Alias
    UMLS CUI [1,1]
    C2348585 (Clinical Trial Subject Unique Identifier)
    Consent group as determined by DAC
    Beschrijving

    CONSENT

    Datatype

    text

    Alias
    UMLS CUI [1,1]
    C0021430 (Informed Consent)
    UMLS CUI [1,2]
    C0441833 (Groups)
    SNOMED
    246261001
    Case control status of the subject for hypodiploid pre-B acute lymphoblastic leukemia status post matched unrelated donor allogeneic hematopoietic stem cell transplant complicated by fulminant myocarditis on day +75
    Beschrijving

    AFFECTION_STATUS

    Datatype

    text

    Alias
    UMLS CUI [1,1]
    C3274646 (Participant Case or Control Status)

    Similar models

    The subject consent data table contains patient IDs, consent group information, and affection status of subject for hypodiploid pre-B acute lymphoblastic leukemia status post matched unrelated donor allogeneic hematopoietic stem cell transplant complicated by fulminant myocarditis on day +75.

    Name
    Type
    Description | Question | Decode (Coded Value)
    Datatype
    Alias
    Item Group
    pht006204
    C3846158 (UMLS CUI [1,1])
    PatientID
    Item
    Subject ID
    string
    C2348585 (UMLS CUI [1,1])
    Item
    Consent group as determined by DAC
    text
    C0021430 (UMLS CUI [1,1])
    C0441833 (UMLS CUI [1,2])
    Code List
    Consent group as determined by DAC
    CL Item
    Health/Medical/Biomedical (IRB, PUB, COL, MDS, GSO) (HMB-IRB-PUB-COL-MDS-GSO) (2)
    Item
    Case control status of the subject for hypodiploid pre-B acute lymphoblastic leukemia status post matched unrelated donor allogeneic hematopoietic stem cell transplant complicated by fulminant myocarditis on day +75
    text
    C3274646 (UMLS CUI [1,1])
    Code List
    Case control status of the subject for hypodiploid pre-B acute lymphoblastic leukemia status post matched unrelated donor allogeneic hematopoietic stem cell transplant complicated by fulminant myocarditis on day +75
    CL Item
    Control (1)
    C3274648 (UMLS CUI [1,1])
    CL Item
    Case (2)
    C3274647 (UMLS CUI [1,1])
    CL Item
    Other (3)

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