ID

45226

Description

Principal Investigator: Junko Oshima, MD, PhD, Department of Pathology, University of Washington, Seattle, WA, USA MeSH: Werner Syndrome https://www.ncbi.nlm.nih.gov/projects/gap/cgi-bin/study.cgi?study_id=phs000434 Werner syndrome (WS) is an adult-onset progeroid syndrome characterized by accelerated aging. The International Registry of Werner Syndrome in the Department of Pathology, University of Washington, collects WS cases from all over the world. Classical WS is caused by WRN mutations. Those who do not carry *WRN* are categorized as "atypical Werner syndrome." A small subset of atypical WS is caused by *LMNA* mutations. There also are many cases whose causes are still unknown. The purpose of this study is to identify other causative gene(s) of atypical WS.

Link

dbGaP study = phs000434

Keywords

  1. 7/29/22 7/29/22 - Simon Heim
  2. 10/12/22 10/12/22 - Adrian Schulz
Copyright Holder

Junko Oshima, MD, PhD, Department of Pathology, University of Washington, Seattle, WA, USA

Uploaded on

October 12, 2022

DOI

To request one please log in.

License

Creative Commons BY 4.0

Model comments :

You can comment on the data model here. Via the speech bubbles at the itemgroups and items you can add comments to those specificially.

Itemgroup comments for :

Item comments for :

In order to download data models you must be logged in. Please log in or register for free.

dbGaP phs000434 Next Generation Mendelian Genetics: Atypical Werner Syndrome

Eligibility Criteria

Inclusion and exclusion criteria
Description

Inclusion and exclusion criteria

Inclusion to the study is based on the clinical criteria of Werner syndrome ( http://www.wernersyndrome.org/registry/diagnostic.html). Those who have *WRN* mutations and *LMN* mutations are excluded.
Description

Inclusion to the study is based on the clinical criteria of Werner syndrome. Those who have *WRN* mutations and *LMN* mutations are excluded.

Data type

boolean

Alias
UMLS CUI [1,1]
C0680251
UMLS CUI [1,2]
C1711435
UMLS CUI [1,3]
C0524459
UMLS CUI [1,4]
C0026882
UMLS CUI [2,1]
C1512693
UMLS CUI [2,2]
C0043119

Similar models

Eligibility Criteria

Name
Type
Description | Question | Decode (Coded Value)
Data type
Alias
Item Group
Inclusion and exclusion criteria
Inclusion to the study is based on the clinical criteria of Werner syndrome. Those who have *WRN* mutations and *LMN* mutations are excluded.
Item
Inclusion to the study is based on the clinical criteria of Werner syndrome ( http://www.wernersyndrome.org/registry/diagnostic.html). Those who have *WRN* mutations and *LMN* mutations are excluded.
boolean
C0680251 (UMLS CUI [1,1])
C1711435 (UMLS CUI [1,2])
C0524459 (UMLS CUI [1,3])
C0026882 (UMLS CUI [1,4])
C1512693 (UMLS CUI [2,1])
C0043119 (UMLS CUI [2,2])

Please use this form for feedback, questions and suggestions for improvements.

Fields marked with * are required.

Do you need help on how to use the search function? Please watch the corresponding tutorial video for more details and learn how to use the search function most efficiently.

Watch Tutorial