0 Avaliações

ID

45223

Descrição

Principal Investigator: James R. Downing, MD, Dept. of Pathology, St. Jude Children's Research Hospital, Memphis, TN, USA MeSH: Acute Myeloid Leukemia https://www.ncbi.nlm.nih.gov/projects/gap/cgi-bin/study.cgi?study_id=phs000414 Pediatric *de novo* acute myeloid leukemia (AML) is a heterogeneous disease that can be divided into clinically distinct subtypes based on the presence of specific chromosomal abnormalities or gene alterations. One of the best characterized subtypes of AML involves leukemias with alterations of the core-binding factor (CBF)-complex, which comprises the FAB subtypes M2 and M4Eo and associates with a favorable outcome. Patients with the AML M2 subtype harbor a translocation between chromosomes 8 and 21 [t(8;21)] that yields the chimeric fusion gene *RUNX1(AML1)-RUNX1T1(ETO)*, while patients with AML M4Eo express the chimeric fusion gene *CBFβ-SMMHC(MYH11)* as a result of an inversion/translocation event of chromosome 16 [inv(16)/t(16;16)]. In an effort to define the total complement of genetic changes in CBF-leukemia, we performed paired-end whole genome sequencing (WGS) on diagnostic leukemia blasts and matched germ line samples from 17 pediatric CBF-leukemia patients using the Illumina platform. Somatic alterations, including single nucleotide variations (SNVs) and structural variations (SVs), including insertions, deletions, inversions, and inter- and intra-chromosomal rearrangements, were detected using complementary analysis pipelines (Bambino, CREST and CONSERTING). Recurrent screening of identified mutations will be performed in a cohort of approximately 94 cases of CBF-leukemias.

Link

dbGaP study = phs000414

Palavras-chave

  1. 29/07/2022 29/07/2022 - Simon Heim
  2. 12/10/2022 12/10/2022 - Adrian Schulz
Titular dos direitos

James R. Downing, MD, Dept. of Pathology, St. Jude Children's Research Hospital, Memphis, TN, USA

Transferido a

12 de outubro de 2022

DOI

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Licença

Creative Commons BY 4.0

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    dbGaP phs000414 Whole Genome Sequencing of CBF-Leukemia

    Subject ID, subject source, subject source ID, consent groups, and affection status of participants with leukemia and involved in the "Whole genome sequencing of core-binding factor leukemia" project.

    pht002729
    Descrição

    pht002729

    Subject ID
    Descrição

    SUBJID

    Tipo de dados

    string

    Alias
    UMLS CUI [1,1]
    C2348585
    Consent group as determined by DAC
    Descrição

    CONSENT

    Tipo de dados

    text

    Alias
    UMLS CUI [1,1]
    C0021430
    UMLS CUI [1,2]
    C1257890
    Source repository where subjects originate
    Descrição

    SUBJ_SOURCE

    Tipo de dados

    string

    Alias
    UMLS CUI [1,1]
    C0449416
    UMLS CUI [1,2]
    C3847505
    Subject ID used in the Source Repository
    Descrição

    SOURCE_SUBJID

    Tipo de dados

    string

    Alias
    UMLS CUI [1,1]
    C2348585
    UMLS CUI [1,2]
    C0449416
    UMLS CUI [1,3]
    C3847505
    Case control status of the subject
    Descrição

    AFFECTION_STATUS

    Tipo de dados

    text

    Alias
    UMLS CUI [1,1]
    C3274646

    Similar models

    Subject ID, subject source, subject source ID, consent groups, and affection status of participants with leukemia and involved in the "Whole genome sequencing of core-binding factor leukemia" project.

    Name
    Tipo
    Description | Question | Decode (Coded Value)
    Tipo de dados
    Alias
    Item Group
    pht002729
    SUBJID
    Item
    Subject ID
    string
    C2348585 (UMLS CUI [1,1])
    Item
    Consent group as determined by DAC
    text
    C0021430 (UMLS CUI [1,1])
    C1257890 (UMLS CUI [1,2])
    Code List
    Consent group as determined by DAC
    CL Item
    General Research Use (GRU) (1)
    SUBJ_SOURCE
    Item
    Source repository where subjects originate
    string
    C0449416 (UMLS CUI [1,1])
    C3847505 (UMLS CUI [1,2])
    SOURCE_SUBJID
    Item
    Subject ID used in the Source Repository
    string
    C2348585 (UMLS CUI [1,1])
    C0449416 (UMLS CUI [1,2])
    C3847505 (UMLS CUI [1,3])
    Item
    Case control status of the subject
    text
    C3274646 (UMLS CUI [1,1])
    Code List
    Case control status of the subject
    CL Item
    Case (2)

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