0 Avaliações

ID

45173

Descrição

Principal Investigator: James R. Downing, MD, Dept. of Pathology, St. Jude Children' Research Hospital, Memphis, TN, USA MeSH: Acute Megakaryoblastic Leukemia,Acute Myeloid Leukemia https://www.ncbi.nlm.nih.gov/projects/gap/cgi-bin/study.cgi?study_id=phs000413 High resolution analysis of DNA copy number abnormalities and loss-of-heterozygosity on acute myeloblastic leukemia samples utilizing SNP arrays has demonstrated that in contrast to pediatric ALL, de novo AML is characterized by a very low burden of genomic alterations (Radtke, et al., PNAS, 2009). Samples for this study represented a cross-section of the different subtypes of pediatric AML. The only AML subtype that was an outlier from the above observations was acute megakaryocytic leukemia (AML FAB-M7), with the majority of these cases being characterized by complex chromosomal rearrangements and a high number of copy number alterations. To more fully define the genomic landscape of this subtype, we performed transcriptome sequence analysis on 14 pediatric FAB-M7 cases and mutation recurrence screening in a panel of 62 adult and pediatric AML FAB-M7 samples using the Illumina platform. Our results identified chromosomal rearrangements resulting in the expression of novel fusion transcripts in 11/14 cases. Remarkably, in 7/14 cases we detected an inversion on chromosome 16 that results in the juxtaposition of the CBFA2T3 gene next to the GLIS2 gene resulting in a CBFA2T3-GLIS2 chimeric gene that encoded an in frame fusion protein. This fusion led to the acquisition or preservation of self-renewal in colony forming assays, providing functional evidence for a role in leukemogenesis. In addition to novel chimeric transcripts, we found mutations in genes previously identified to play a role in megakaryoblastic leukemia that carry a proliferative advantage to the cell, such as JAK2 and MPL. These data demonstrate that AML FAB-M7 is characterized by cooperating Class I and Class II mutations leading to leukemogenesis.

Link

dbGaP study = phs000413

Palavras-chave

  1. 22/08/2022 22/08/2022 - Niko Möller-Grell
  2. 12/10/2022 12/10/2022 - Adrian Schulz
Titular dos direitos

James R. Downing, MD, Dept. of Pathology, St. Jude Children' Research Hospital, Memphis, TN, USA

Transferido a

12 de outubro de 2022

DOI

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Licença

Creative Commons BY 4.0

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    dbGaP phs000413 Transcriptome Sequencing of Pediatric AML FAB-M7

    Subject ID, age at diagnosis, ethnicity, gender, relapse and vital status, if patient receive a bone marrow transplant, primary treatment protocol, disease code, genetic lesions, characteristic of specimen including tumor purity, type of specimen, and tissue site where from the specimen was obtained from participants with acute myeloblastic leukemia and involved in the "Analysis of Somatic Mutations in Pediatric AML FAB-M7 Subtype by Whole Transcriptome Sequencing" project.

    1. StudyEvent: SEV1
      1. Eligibility Criteria
      2. Subject ID, consent group, subject source, subject source ID, and affection status of participants with acute myeloblastic leukemia and involved in the "Analysis of Somatic Mutations in Pediatric AML FAB-M7 Subtype by Whole Transcriptome Sequencing" project.
      3. Sample ID, subject ID, sample source, sample source ID, and sample use variables obtained from participants with acute myeloblastic leukemia and involved in the "Analysis of Somatic Mutations in Pediatric AML FAB-M7 Subtype by Whole Transcriptome Sequencing" project.
      4. Sample ID, body site where sample was collected, analyte type of samples, tumor status, histological type of samples, and primary tumor location obtained from participants with acute myeloblastic leukemia and involved in the "Analysis of Somatic Mutations in Pediatric AML FAB-M7 Subtype by Whole Transcriptome Sequencing" project.
      5. Subject ID, age at diagnosis, ethnicity, gender, relapse and vital status, if patient receive a bone marrow transplant, primary treatment protocol, disease code, genetic lesions, characteristic of specimen including tumor purity, type of specimen, and tissue site where from the specimen was obtained from participants with acute myeloblastic leukemia and involved in the "Analysis of Somatic Mutations in Pediatric AML FAB-M7 Subtype by Whole Transcriptome Sequencing" project.
      6. Sample ID and GEO accession ID of participants with acute myeloblastic leukemia and involved in the "Analysis of Somatic Mutations in Pediatric AML FAB-M7 Subtype by Whole Transcriptome Sequencing" project.
    pht003037
    Descrição

    pht003037

    De-identified subject's ID
    Descrição

    SUBJID

    Tipo de dados

    text

    Alias
    UMLS CUI [1,1]
    C4684638
    UMLS CUI [1,2]
    C2348585
    Age at Diagnosis (Years)
    Descrição

    ageAtDxYears

    Tipo de dados

    integer

    Unidades de medida
    • Years
    Alias
    UMLS CUI [1,1]
    C0001779
    UMLS CUI [1,2]
    C0011900
    Years
    Additional Info (usually regarding Molecular Testing)
    Descrição

    additionalInfo

    Tipo de dados

    string

    Alias
    UMLS CUI [1,1]
    C1546922
    Primary treatment protocol [AML97, AML02, AML91, AML86/AML87]
    Descrição

    primaryProtocol

    Tipo de dados

    text

    Alias
    UMLS CUI [1,1]
    C1708063
    Did the patient relapse?
    Descrição

    relapse

    Tipo de dados

    text

    Alias
    UMLS CUI [1,1]
    C0699753
    Did the patient receive a bone marrow transplant?
    Descrição

    bmt

    Tipo de dados

    text

    Alias
    UMLS CUI [1,1]
    C0005961
    Genetic lesions
    Descrição

    geneticLesions

    Tipo de dados

    string

    Alias
    UMLS CUI [1,1]
    C0314603
    UMLS CUI [1,2]
    C0221198
    Gender
    Descrição

    gender

    Tipo de dados

    text

    Alias
    UMLS CUI [1,1]
    C0079399
    Ethnicity
    Descrição

    ethnicity

    Tipo de dados

    text

    Alias
    UMLS CUI [1,1]
    C0015031
    Vital status
    Descrição

    vitalStatus

    Tipo de dados

    text

    Alias
    UMLS CUI [1,1]
    C3846084
    Tumor purity
    Descrição

    tumorPurity

    Tipo de dados

    string

    Alias
    UMLS CUI [1,1]
    C4288090
    Disease code AMLM7
    Descrição

    diseaseCode

    Tipo de dados

    text

    Alias
    UMLS CUI [1,1]
    C0279632
    Type of specimen
    Descrição

    typeOfSpecimen

    Tipo de dados

    text

    Alias
    UMLS CUI [1,1]
    C0456204
    Tissue site [Bone Marrow, Peripheral Blood]
    Descrição

    tissueSite

    Tipo de dados

    text

    Alias
    UMLS CUI [1,1]
    C0200345
    UMLS CUI [1,2]
    C1545955

    Similar models

    Subject ID, age at diagnosis, ethnicity, gender, relapse and vital status, if patient receive a bone marrow transplant, primary treatment protocol, disease code, genetic lesions, characteristic of specimen including tumor purity, type of specimen, and tissue site where from the specimen was obtained from participants with acute myeloblastic leukemia and involved in the "Analysis of Somatic Mutations in Pediatric AML FAB-M7 Subtype by Whole Transcriptome Sequencing" project.

    1. StudyEvent: SEV1
      1. Eligibility Criteria
      2. Subject ID, consent group, subject source, subject source ID, and affection status of participants with acute myeloblastic leukemia and involved in the "Analysis of Somatic Mutations in Pediatric AML FAB-M7 Subtype by Whole Transcriptome Sequencing" project.
      3. Sample ID, subject ID, sample source, sample source ID, and sample use variables obtained from participants with acute myeloblastic leukemia and involved in the "Analysis of Somatic Mutations in Pediatric AML FAB-M7 Subtype by Whole Transcriptome Sequencing" project.
      4. Sample ID, body site where sample was collected, analyte type of samples, tumor status, histological type of samples, and primary tumor location obtained from participants with acute myeloblastic leukemia and involved in the "Analysis of Somatic Mutations in Pediatric AML FAB-M7 Subtype by Whole Transcriptome Sequencing" project.
      5. Subject ID, age at diagnosis, ethnicity, gender, relapse and vital status, if patient receive a bone marrow transplant, primary treatment protocol, disease code, genetic lesions, characteristic of specimen including tumor purity, type of specimen, and tissue site where from the specimen was obtained from participants with acute myeloblastic leukemia and involved in the "Analysis of Somatic Mutations in Pediatric AML FAB-M7 Subtype by Whole Transcriptome Sequencing" project.
      6. Sample ID and GEO accession ID of participants with acute myeloblastic leukemia and involved in the "Analysis of Somatic Mutations in Pediatric AML FAB-M7 Subtype by Whole Transcriptome Sequencing" project.
    Name
    Tipo
    Description | Question | Decode (Coded Value)
    Tipo de dados
    Alias
    Item Group
    pht003037
    SUBJID
    Item
    De-identified subject's ID
    text
    C4684638 (UMLS CUI [1,1])
    C2348585 (UMLS CUI [1,2])
    ageAtDxYears
    Item
    Age at Diagnosis (Years)
    integer
    C0001779 (UMLS CUI [1,1])
    C0011900 (UMLS CUI [1,2])
    additionalInfo
    Item
    Additional Info (usually regarding Molecular Testing)
    string
    C1546922 (UMLS CUI [1,1])
    primaryProtocol
    Item
    Primary treatment protocol [AML97, AML02, AML91, AML86/AML87]
    text
    C1708063 (UMLS CUI [1,1])
    Item
    Did the patient relapse?
    text
    C0699753 (UMLS CUI [1,1])
    Code List
    Did the patient relapse?
    CL Item
    Yes (Y)
    CL Item
    No (N)
    CL Item
    Persistent disease (PD)
    CL Item
    Unknown (UN)
    Item
    Did the patient receive a bone marrow transplant?
    text
    C0005961 (UMLS CUI [1,1])
    Code List
    Did the patient receive a bone marrow transplant?
    CL Item
    Yes (Y)
    CL Item
    No (N)
    CL Item
    Unknown (UN)
    geneticLesions
    Item
    Genetic lesions
    string
    C0314603 (UMLS CUI [1,1])
    C0221198 (UMLS CUI [1,2])
    Item
    Gender
    text
    C0079399 (UMLS CUI [1,1])
    Code List
    Gender
    CL Item
    Male (M)
    CL Item
    Female (F)
    Item
    Ethnicity
    text
    C0015031 (UMLS CUI [1,1])
    Code List
    Ethnicity
    CL Item
    White (W)
    CL Item
    Black (B)
    CL Item
    No Data (ND)
    Item
    Vital status
    text
    C3846084 (UMLS CUI [1,1])
    Code List
    Vital status
    CL Item
    Alive (A)
    CL Item
    Deceased (D)
    CL Item
    Unknown (UN)
    tumorPurity
    Item
    Tumor purity
    string
    C4288090 (UMLS CUI [1,1])
    diseaseCode
    Item
    Disease code AMLM7
    text
    C0279632 (UMLS CUI [1,1])
    Item
    Type of specimen
    text
    C0456204 (UMLS CUI [1,1])
    Code List
    Type of specimen
    CL Item
    DNA (DNA)
    CL Item
    DNA, RNA (DNA, RNA)
    tissueSite
    Item
    Tissue site [Bone Marrow, Peripheral Blood]
    text
    C0200345 (UMLS CUI [1,1])
    C1545955 (UMLS CUI [1,2])

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